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罕见,深圳发现一例“镜面人”

  • 2026-05-23 10:53:45
罕见,深圳发现一例“镜面人”
近日
深圳发现一例罕见镜面人
39岁女子气喘就医
发现内脏全长反
与正常人完全“镜像翻转”

近日,深圳市人民医院心脏大血管外科成功完成一例具有里程碑意义的高难度微创心脏手术——全3D胸腔镜下镜面右位心二尖瓣修复术。经文献检索,国际上已有全3D胸腔镜下右位心患者二尖瓣置换手术的个案报道,但全3D胸腔镜下为镜面右位心、二尖瓣脱垂患者实施二尖瓣修复手术极为罕见,这标志着医院在微创心脏外科和罕见病外科治疗领域达到了新高度。

▲术前CTA提示全内脏反位。

心脏“长反了”,瓣膜也坏了

39岁的患者李女士因“活动后气促1月余”入住深圳市人民医院心脏大血管外科。入院后超声心动图提示:二尖瓣脱垂伴重度关闭不全——通俗地说,就是心脏的“阀门”坏了,关不严了。

然而,并不只是瓣膜出了问题。影像学检查还揭示了一个更为罕见的事实:李女士是全内脏反位患者,也就是俗称的“镜面人”。与常人相反,她的心脏位于右侧胸腔(镜面右位心),肝脏位于左侧。这种先天性结构异常的发生率约为1/8000至1/10000,而其中合并二尖瓣脱垂需手术干预者更是少之又少。当“长反了的心脏”遇上“坏了的瓣膜”,一场前所未有的高难度手术由此拉开序幕。

左位换右位,挑战禁忌

传统二尖瓣修复术在解剖结构正常的心脏上已是精细操作,而面对这位“镜面人”患者,一切都变得与众不同。

人体的心脏如同一栋精密的“房子”,医生需要在其内部进行精细操作。然而,当所有结构完全镜像反转后,医生的每一步操作都意味着打破数十年的肌肉记忆:不仅解剖位置相反,手术器械的操作方向、术者站位、影像判读均需彻底“反向思维”。任何按照常规逻辑的动作,都可能引发灾难性后果。

面对这一挑战,深圳市人民医院心脏大血管外科在科主任郑奇军的带领下,组织全科力量进行了多次术前讨论和多学科会诊。手术由孟春营主任医师主刀,一助李大刚副主任医师、二助王秋吉住院医师密切配合,术中体外循环由赵萍主任医师、廖雅琳主治医师负责,为手术的平稳实施提供了关键保障。在超声科、麻醉科和手术室的全力支持下,一场精密的手术拉开帷幕。手术中,团队采用全3D胸腔镜微创技术。患者无需正中开胸,仅通过右侧胸壁几个小孔即可在高清3D视野下精准辨认“镜像”解剖关系,以反向入路完成了对脱垂二尖瓣的修复,恢复了瓣膜的启闭功能,手术取得圆满成功。

术后,患者转入重症监护室。在覃庚亮主治医师的医疗监护下,曾碧茹护士长统筹护理方案,由陈月儿主管护师等人组成的专业护理团队落实各项精细化术后护理措施;在医护紧密协作下,患者恢复过程平稳顺利。术后复查超声心动图显示:二尖瓣修复效果满意,瓣膜活动良好,未见任何返流。

从“换瓣”到“修瓣”,理念的跨越

为什么主刀团队坚持选择“修复”而非“置换”?这不仅是技术难度的选择,更是治疗理念的跨越。二尖瓣修复术相较于人工瓣膜置换,能最大程度保留患者自身的瓣膜结构和心脏功能,不仅远期生存率显著优于置换术,而且术后无需终身抗凝,生活质量更高。对于年仅39岁的李女士而言,修复即意味着终身的获益。而在镜面右位心的复杂背景下成功完成经3D全胸腔镜下的修复,且为国内首例报道、国际罕见,更体现了医院心脏大血管外科团队过硬的技术实力和对患者长远预后的担当。

修瓣和换瓣有什么区别?二尖瓣置换是用人工瓣膜替代原有瓣膜,手术路径相对直接,但患者术后可能面临长期抗凝、人工瓣膜相关并发症等问题。二尖瓣修复则是在保留自身瓣膜的基础上恢复其正常功能,对医生技术要求更高。对于年轻患者而言,成功修复通常意味着更接近生理状态的心脏功能和更好的长期生活质量。

医生提醒

如反复出现活动后

气促、胸闷、心悸、乏力

或体检发现心脏杂音

心脏扩大、瓣膜返流等情况

应及时到心脏专科进一步评估

早期发现、规范随访和适时干预

是改善瓣膜病长期预后的关键

来源:南方+、第一现场、深圳市人民医院

编辑:吴俊霞、郭含笑

校审:施冰冰、吴沁彤郑创彬

转载请注明

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  1. CONNECT:[ UseTime:0.000627s ] mysql:host=127.0.0.1;port=3306;dbname=c460;charset=utf8mb4
  2. SHOW FULL COLUMNS FROM `fenlei` [ RunTime:0.000848s ]
  3. SELECT * FROM `fenlei` WHERE `fid` = 0 [ RunTime:0.000319s ]
  4. SELECT * FROM `fenlei` WHERE `fid` = 63 [ RunTime:0.000272s ]
  5. SHOW FULL COLUMNS FROM `set` [ RunTime:0.000592s ]
  6. SELECT * FROM `set` [ RunTime:0.000255s ]
  7. SHOW FULL COLUMNS FROM `article` [ RunTime:0.000646s ]
  8. SELECT * FROM `article` WHERE `id` = 592980 LIMIT 1 [ RunTime:0.002709s ]
  9. UPDATE `article` SET `lasttime` = 1779736133 WHERE `id` = 592980 [ RunTime:0.019644s ]
  10. SELECT * FROM `fenlei` WHERE `id` = 64 LIMIT 1 [ RunTime:0.000433s ]
  11. SELECT * FROM `article` WHERE `id` < 592980 ORDER BY `id` DESC LIMIT 1 [ RunTime:0.000655s ]
  12. SELECT * FROM `article` WHERE `id` > 592980 ORDER BY `id` ASC LIMIT 1 [ RunTime:0.000458s ]
  13. SELECT * FROM `article` WHERE `id` < 592980 ORDER BY `id` DESC LIMIT 10 [ RunTime:0.001887s ]
  14. SELECT * FROM `article` WHERE `id` < 592980 ORDER BY `id` DESC LIMIT 10,10 [ RunTime:0.003573s ]
  15. SELECT * FROM `article` WHERE `id` < 592980 ORDER BY `id` DESC LIMIT 20,10 [ RunTime:0.001539s ]
0.107352s